Hb D/Talassemia beta associada à anemia crônica

We describe a case of Hb D/Beta thalassemia associated with chronic anemia. Hematological analyses performed in a patient with chronic anemia demonstrating microcytosis and hypochromic in his erythrocytes. Specific laboratory diagnosis performed by alkaline and acid electrophoresis, and fetal determination by alkali resistance, indicated it to be Hb D associated with beta thalassemia. Analyses carried out on his family (father, mother and brother) confirmed the suspected diagnosis. Hb D/Beta thalassemia is a very rare interaction in the Brazilian population, and its determination required specific laboratorial techniques and hematological analyses.

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Detalhes bibliográficos
Principais autores: Naoum,Paulo C., Moraes,Magaly S., Radispiel,Janaína, Cavalheri,Priscila P., Valeri,Fábio F.
Formato: Digital revista
Idioma:Portuguese
Publicado em: Associação Brasileira de Hematologia e Hemoterapia e Terapia Celular 2002
Acesso em linha:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1516-84842002000100010
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