Endovascular treatment of intrarenal aneurysms bleeding and angiomyolipomas in a patient with tuberous sclerosis and polycystic kidney disease

Abstract Tuberous sclerosis complex (TSC) and autosomal dominant polycystic kidney disease (ADPKD) are conditions related to renal failure that can rarely occur in association as a contiguous gene syndrome. Angiomyolipomas (AMLs) are renal tumors strongly related to TSC that may rupture and cause life-threatening bleedings. We present a patient with TSC, ADPKD, and renal AMLs with persistent hematuria requiring blood transfusion. The persistent hematuria was successfully treated through endovascular embolization, a minimally invasive nephron sparing technique.

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Auteurs principaux: Leite,Túlio, Pazinato,Lucas Vatanabe, Vidal,Maria Juliana de Aquino, Freitas,Danielo de, Leal Filho,Joaquim Mauricio da Motta
Format: Digital revista
Langue:English
Publié: Sociedade Brasileira de Nefrologia 2021
Accès en ligne:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0101-28002021005062301
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