Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation

Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation

Abstract Only a few cases of peripheral Primary Neuroectodermal Tumor (pPNET) arising in the rectum have been described in the literature. We report a case of a 54-year- old male patient with urinary retention and lower abdominal pain, whose CT and MRI demonstrated a pelvic mass compressing the rectum and bladder. After surgical resection, histologic and immunohistochemical findings were compatible with a rectal pPNET, with a proliferation index of 10%. This case draws the attention to a rare and aggressive condition that has no specific symptoms or typical imaging features, consisting of a rapid growing tumor with poor prognosis, even after surgical resection and chemotherapy.

Saved in:
Bibliographic Details
Main Authors: Freire1,Gonçalo, Mira1,Catarina, Primitivo1,Ana, Sousa1,Pedro, Madureira2,Rosa, Valentim,Maria Helena
Format: Digital revista
Language:English
Published: Sociedade Portuguesa de Radiologia e Medicina Nuclear 2020
Online Access:http://scielo.pt/scielo.php?script=sci_arttext&pid=S2183-13512020000100019
Tags: Add Tag
No Tags, Be the first to tag this record!
id oai:scielo:S2183-13512020000100019
record_format ojs
spelling oai:scielo:S2183-135120200001000192021-10-25Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological CorrelationFreire1,GonçaloMira1,CatarinaPrimitivo1,AnaSousa1,PedroMadureira2,RosaValentim,Maria Helena Peripheral primitive neuroectodermal tumor Computed tomography Magnetic resonance imaging. Abstract Only a few cases of peripheral Primary Neuroectodermal Tumor (pPNET) arising in the rectum have been described in the literature. We report a case of a 54-year- old male patient with urinary retention and lower abdominal pain, whose CT and MRI demonstrated a pelvic mass compressing the rectum and bladder. After surgical resection, histologic and immunohistochemical findings were compatible with a rectal pPNET, with a proliferation index of 10%. This case draws the attention to a rare and aggressive condition that has no specific symptoms or typical imaging features, consisting of a rapid growing tumor with poor prognosis, even after surgical resection and chemotherapy.info:eu-repo/semantics/openAccessSociedade Portuguesa de Radiologia e Medicina NuclearActa Radiológica Portuguesa v.32 n.1 20202020-04-01info:eu-repo/semantics/reporttext/htmlhttp://scielo.pt/scielo.php?script=sci_arttext&pid=S2183-13512020000100019en10.25748/arp.18113
institution SCIELO
collection OJS
country Portugal
countrycode PT
component Revista
access En linea
databasecode rev-scielo-pt
tag revista
region Europa del Sur
libraryname SciELO
language English
format Digital
author Freire1,Gonçalo
Mira1,Catarina
Primitivo1,Ana
Sousa1,Pedro
Madureira2,Rosa
Valentim,Maria Helena
spellingShingle Freire1,Gonçalo
Mira1,Catarina
Primitivo1,Ana
Sousa1,Pedro
Madureira2,Rosa
Valentim,Maria Helena
Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation
author_facet Freire1,Gonçalo
Mira1,Catarina
Primitivo1,Ana
Sousa1,Pedro
Madureira2,Rosa
Valentim,Maria Helena
author_sort Freire1,Gonçalo
title Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation
title_short Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation
title_full Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation
title_fullStr Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation
title_full_unstemmed Rectal Peripheral Primitive Neuroectodermal Tumor: Case Report and Radio-Pathological Correlation
title_sort rectal peripheral primitive neuroectodermal tumor: case report and radio-pathological correlation
description Abstract Only a few cases of peripheral Primary Neuroectodermal Tumor (pPNET) arising in the rectum have been described in the literature. We report a case of a 54-year- old male patient with urinary retention and lower abdominal pain, whose CT and MRI demonstrated a pelvic mass compressing the rectum and bladder. After surgical resection, histologic and immunohistochemical findings were compatible with a rectal pPNET, with a proliferation index of 10%. This case draws the attention to a rare and aggressive condition that has no specific symptoms or typical imaging features, consisting of a rapid growing tumor with poor prognosis, even after surgical resection and chemotherapy.
publisher Sociedade Portuguesa de Radiologia e Medicina Nuclear
publishDate 2020
url http://scielo.pt/scielo.php?script=sci_arttext&pid=S2183-13512020000100019
work_keys_str_mv AT freire1goncalo rectalperipheralprimitiveneuroectodermaltumorcasereportandradiopathologicalcorrelation
AT mira1catarina rectalperipheralprimitiveneuroectodermaltumorcasereportandradiopathologicalcorrelation
AT primitivo1ana rectalperipheralprimitiveneuroectodermaltumorcasereportandradiopathologicalcorrelation
AT sousa1pedro rectalperipheralprimitiveneuroectodermaltumorcasereportandradiopathologicalcorrelation
AT madureira2rosa rectalperipheralprimitiveneuroectodermaltumorcasereportandradiopathologicalcorrelation
AT valentimmariahelena rectalperipheralprimitiveneuroectodermaltumorcasereportandradiopathologicalcorrelation
_version_ 1756003952595304448

Similar Items