Bilateral hearing loss as an initial presentation of Creutzfeldt-Jakob disease

ABSTRACT. We reported a case of a 61-year-old male patient with anacusis, cerebellar syndrome, myoclonus, and frontal signs. The brain magnetic resonance imaging showed bilateral striated hyperintensity of the fluid-attenuated inversion recovery and restricted diffusion in the diffusion-weighted imaging and hypointense areas corresponding to the apparent diffusion coefficient in the cerebral cortex. The autopsy revealed positive immunohistochemistry for the PrPSc protein. Creutzfeldt–Jakob disease presenting with hearing loss is unusual.

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Auteurs principaux: Brito-Marques,Janaina Mariana de Araujo Miranda, Melo,Eduardo Sousa de, Medeiros,Fabíola Lys de, Carvalho,Cristiano Sobral de, Brito-Marques,Paulo Roberto de
Format: Digital revista
Langue:English
Publié: Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento 2021
Accès en ligne:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642021000400548
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