Basal ganglia lesions in subacute sclerosing panencephalitis
ABSTRACT The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia.
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Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento
2012
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oai:scielo:S1980-576420120004002862016-07-15Basal ganglia lesions in subacute sclerosing panencephalitisAlmeida,Kelson JamesBrucki,Sonia Maria DozziDuarte,Maria Irma SeixasPasqualucci,Carlos Augusto GonçalvesRosemberg,SérgioNitrini,Ricardo subacute sclerosing panencephalitis measles magnetic resonance imaging ABSTRACT The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia.info:eu-repo/semantics/openAccessAcademia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e EnvelhecimentoDementia & Neuropsychologia v.6 n.4 20122012-12-01info:eu-repo/semantics/reporttext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642012000400286en10.1590/S1980-57642012DN06040014 |
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Almeida,Kelson James Brucki,Sonia Maria Dozzi Duarte,Maria Irma Seixas Pasqualucci,Carlos Augusto Gonçalves Rosemberg,Sérgio Nitrini,Ricardo |
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Almeida,Kelson James Brucki,Sonia Maria Dozzi Duarte,Maria Irma Seixas Pasqualucci,Carlos Augusto Gonçalves Rosemberg,Sérgio Nitrini,Ricardo Basal ganglia lesions in subacute sclerosing panencephalitis |
author_facet |
Almeida,Kelson James Brucki,Sonia Maria Dozzi Duarte,Maria Irma Seixas Pasqualucci,Carlos Augusto Gonçalves Rosemberg,Sérgio Nitrini,Ricardo |
author_sort |
Almeida,Kelson James |
title |
Basal ganglia lesions in subacute sclerosing panencephalitis |
title_short |
Basal ganglia lesions in subacute sclerosing panencephalitis |
title_full |
Basal ganglia lesions in subacute sclerosing panencephalitis |
title_fullStr |
Basal ganglia lesions in subacute sclerosing panencephalitis |
title_full_unstemmed |
Basal ganglia lesions in subacute sclerosing panencephalitis |
title_sort |
basal ganglia lesions in subacute sclerosing panencephalitis |
description |
ABSTRACT The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia. |
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Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento |
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2012 |
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http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642012000400286 |
work_keys_str_mv |
AT almeidakelsonjames basalganglialesionsinsubacutesclerosingpanencephalitis AT bruckisoniamariadozzi basalganglialesionsinsubacutesclerosingpanencephalitis AT duartemariairmaseixas basalganglialesionsinsubacutesclerosingpanencephalitis AT pasqualuccicarlosaugustogoncalves basalganglialesionsinsubacutesclerosingpanencephalitis AT rosembergsergio basalganglialesionsinsubacutesclerosingpanencephalitis AT nitriniricardo basalganglialesionsinsubacutesclerosingpanencephalitis |
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