Basal ganglia lesions in subacute sclerosing panencephalitis

ABSTRACT The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia.

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Main Authors: Almeida,Kelson James, Brucki,Sonia Maria Dozzi, Duarte,Maria Irma Seixas, Pasqualucci,Carlos Augusto Gonçalves, Rosemberg,Sérgio, Nitrini,Ricardo
Format: Digital revista
Language:English
Published: Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento 2012
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642012000400286
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spelling oai:scielo:S1980-576420120004002862016-07-15Basal ganglia lesions in subacute sclerosing panencephalitisAlmeida,Kelson JamesBrucki,Sonia Maria DozziDuarte,Maria Irma SeixasPasqualucci,Carlos Augusto GonçalvesRosemberg,SérgioNitrini,Ricardo subacute sclerosing panencephalitis measles magnetic resonance imaging ABSTRACT The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia.info:eu-repo/semantics/openAccessAcademia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e EnvelhecimentoDementia & Neuropsychologia v.6 n.4 20122012-12-01info:eu-repo/semantics/reporttext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642012000400286en10.1590/S1980-57642012DN06040014
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countrycode BR
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region America del Sur
libraryname SciELO
language English
format Digital
author Almeida,Kelson James
Brucki,Sonia Maria Dozzi
Duarte,Maria Irma Seixas
Pasqualucci,Carlos Augusto Gonçalves
Rosemberg,Sérgio
Nitrini,Ricardo
spellingShingle Almeida,Kelson James
Brucki,Sonia Maria Dozzi
Duarte,Maria Irma Seixas
Pasqualucci,Carlos Augusto Gonçalves
Rosemberg,Sérgio
Nitrini,Ricardo
Basal ganglia lesions in subacute sclerosing panencephalitis
author_facet Almeida,Kelson James
Brucki,Sonia Maria Dozzi
Duarte,Maria Irma Seixas
Pasqualucci,Carlos Augusto Gonçalves
Rosemberg,Sérgio
Nitrini,Ricardo
author_sort Almeida,Kelson James
title Basal ganglia lesions in subacute sclerosing panencephalitis
title_short Basal ganglia lesions in subacute sclerosing panencephalitis
title_full Basal ganglia lesions in subacute sclerosing panencephalitis
title_fullStr Basal ganglia lesions in subacute sclerosing panencephalitis
title_full_unstemmed Basal ganglia lesions in subacute sclerosing panencephalitis
title_sort basal ganglia lesions in subacute sclerosing panencephalitis
description ABSTRACT The parieto-occipital region of the brain is the most frequently and severely affected in subacute sclerosing panencephalitis (SSPE). The basal ganglia, cerebellum and corpus callosum are less commonly involved. We describe a patient with SSPE confirmed by neuropathology based on brain magnetic resonance imaging showing extensive basal ganglia involvement and no significant involvement of other cortical structures. Though rarely described in SSPE, clinicians should be aware of this involvement. SSPE should be kept in mind when changes in basal ganglia signal are seen on brain magnetic resonance imaging with or without involvement of other regions of the human brain to avoid erroneous etiological diagnosis of other pathologies causing rapidly progressive dementia.
publisher Academia Brasileira de Neurologia, Departamento de Neurologia Cognitiva e Envelhecimento
publishDate 2012
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S1980-57642012000400286
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AT duartemariairmaseixas basalganglialesionsinsubacutesclerosingpanencephalitis
AT pasqualuccicarlosaugustogoncalves basalganglialesionsinsubacutesclerosingpanencephalitis
AT rosembergsergio basalganglialesionsinsubacutesclerosingpanencephalitis
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