Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life
Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.
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Sociedade de Pediatria de São Paulo
2016
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oai:scielo:S0103-058220160003003842016-09-08Congenital intrahepatic portosystemic shunt diagnosed during intrauterine lifeBellettini,Camila VieiraWagner,RafaelaBalzanelo,Aleocídio SetteAndretta,André Luis de SouzaMoura,Arthur Nascimento deFabris,Catia CarolinaGubert,Eduardo Maranhão Prenatal diagnosis Congenital abnormalities CT scan Doppler ultrasound Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed.info:eu-repo/semantics/openAccessSociedade de Pediatria de São PauloRevista Paulista de Pediatria v.34 n.3 20162016-09-01info:eu-repo/semantics/reporttext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384en10.1016/j.rppede.2016.03.016 |
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Bellettini,Camila Vieira Wagner,Rafaela Balzanelo,Aleocídio Sette Andretta,André Luis de Souza Moura,Arthur Nascimento de Fabris,Catia Carolina Gubert,Eduardo Maranhão |
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Bellettini,Camila Vieira Wagner,Rafaela Balzanelo,Aleocídio Sette Andretta,André Luis de Souza Moura,Arthur Nascimento de Fabris,Catia Carolina Gubert,Eduardo Maranhão Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
author_facet |
Bellettini,Camila Vieira Wagner,Rafaela Balzanelo,Aleocídio Sette Andretta,André Luis de Souza Moura,Arthur Nascimento de Fabris,Catia Carolina Gubert,Eduardo Maranhão |
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Bellettini,Camila Vieira |
title |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title_short |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
title_full |
Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
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Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
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Congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
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congenital intrahepatic portosystemic shunt diagnosed during intrauterine life |
description |
Abstract Objective: To report a patient with prenatal diagnosis of portosystemic shunt; a rare condition in humans. Case description: 17-Day-old female infant admitted for investigation of suspected diagnosis of portosystemic shunt, presumed in obstetric ultrasound. The hypothesis was confirmed after abdominal angiography and liver Doppler. Other tests such as echocardiography and electroencephalogram were performed to investigate possible co-morbidities or associated complications, and were normal. We chose conservative shunt treatment, as there were no disease-related complications and this was intrahepatic shunt, which could close spontaneously by the age of 2 years. Comments: Portosystemic shunt can lead to various complications such as hepatic encephalopathy, hypergalactosemia, liver tumors, and hepatopulmonary syndrome. Most diagnoses are done after one month of age, after such complications occur. The prenatal diagnosis of this patient provided greater security for the clinical picture management, as well as regular monitoring, which allows the anticipation of possible complications and perform interventional procedures when needed. |
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Sociedade de Pediatria de São Paulo |
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2016 |
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http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0103-05822016000300384 |
work_keys_str_mv |
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