Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart

Syncope in children is primarily related to vagal hyperreactivity, but ventricular tachycardia (VT) way rarely be seen. Catecholaminergic polymorphic VT is a rare entity that can occur in children without heart disease and with a normal QT interval, which may cause syncope and sudden cardiac death. In this report, we describe the clinical features, treatment, and clinical follow-up of three children with syncope associated with physical effort or emotion and cathecolaminergic polymorphic VT. Symptoms were controlled with beta-blockers, but one patient died suddenly in the fourth year of follow-up. Despite the rare occurrence, catecholaminergic polymorphic VT is an important cause of syncope and sudden death in children with no identified heart disease and normal QT interval.

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Autores principales: Leite,Luiz Roberto, Pereira,Kleber R. Ponzi, Alessi,Sílvio R. B., Paola,Angelo A. V. de
Formato: Digital revista
Idioma:English
Publicado: Sociedade Brasileira de Cardiologia - SBC 2001
Acceso en línea:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2001000100007
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spelling oai:scielo:S0066-782X20010001000072001-02-02Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heartLeite,Luiz RobertoPereira,Kleber R. PonziAlessi,Sílvio R. B.Paola,Angelo A. V. deSyncope in children is primarily related to vagal hyperreactivity, but ventricular tachycardia (VT) way rarely be seen. Catecholaminergic polymorphic VT is a rare entity that can occur in children without heart disease and with a normal QT interval, which may cause syncope and sudden cardiac death. In this report, we describe the clinical features, treatment, and clinical follow-up of three children with syncope associated with physical effort or emotion and cathecolaminergic polymorphic VT. Symptoms were controlled with beta-blockers, but one patient died suddenly in the fourth year of follow-up. Despite the rare occurrence, catecholaminergic polymorphic VT is an important cause of syncope and sudden death in children with no identified heart disease and normal QT interval.info:eu-repo/semantics/openAccessSociedade Brasileira de Cardiologia - SBCArquivos Brasileiros de Cardiologia v.76 n.1 20012001-01-01info:eu-repo/semantics/reporttext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2001000100007en10.1590/S0066-782X2001000100007
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language English
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author Leite,Luiz Roberto
Pereira,Kleber R. Ponzi
Alessi,Sílvio R. B.
Paola,Angelo A. V. de
spellingShingle Leite,Luiz Roberto
Pereira,Kleber R. Ponzi
Alessi,Sílvio R. B.
Paola,Angelo A. V. de
Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart
author_facet Leite,Luiz Roberto
Pereira,Kleber R. Ponzi
Alessi,Sílvio R. B.
Paola,Angelo A. V. de
author_sort Leite,Luiz Roberto
title Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart
title_short Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart
title_full Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart
title_fullStr Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart
title_full_unstemmed Catecholaminergic polymorphic ventricular tachycardia. An important diagnosis in children with syncope and normal heart
title_sort catecholaminergic polymorphic ventricular tachycardia. an important diagnosis in children with syncope and normal heart
description Syncope in children is primarily related to vagal hyperreactivity, but ventricular tachycardia (VT) way rarely be seen. Catecholaminergic polymorphic VT is a rare entity that can occur in children without heart disease and with a normal QT interval, which may cause syncope and sudden cardiac death. In this report, we describe the clinical features, treatment, and clinical follow-up of three children with syncope associated with physical effort or emotion and cathecolaminergic polymorphic VT. Symptoms were controlled with beta-blockers, but one patient died suddenly in the fourth year of follow-up. Despite the rare occurrence, catecholaminergic polymorphic VT is an important cause of syncope and sudden death in children with no identified heart disease and normal QT interval.
publisher Sociedade Brasileira de Cardiologia - SBC
publishDate 2001
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X2001000100007
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