Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment

OBJECTIVE: To report the authors' experience with the anomalous origin of the left coronary artery (AOLCA) from the pulmonary trunk, emphasizing preoperative data, surgical aspects and midterm results of the follow-up. METHODS: Retrospective analysis of 11 patients operated upon at the Royal Brompton Hospital from October, 84 to April, 97. RESULTS: Nine infants had heart failure (HF) and two other children presented with dyspnea and chest pain. All had ECG changes. The echocardiogram identified the anomalous origin of the coronary artery in 7 (64%) patients and hemodynamic studies were performed in 7 patients. All infants were operated upon between the 2nd and 10th month of life. Six patients were treated with aortic reimplantation of the left coronary artery, whereas five were operated upon according to the Takeuchi technique. All patients are alive, with clear improvement of the ECG changes and ventricular function, as evaluated by echocardiography. Two patients operated upon according to the Takeuchi technique required additional surgery due to severe supravalvular pulmonary stenosis. CONCLUSION: AOLCA is a rare disease. Most patients show early signs of severe HF associated with ECG findings. Surgical therapy must be instituted early in the disease, preferentially through aortic implantation of the anomalous coronary artery, with a high possibility of success. Shortly after surgery, clinical and ECG improvement, as well as normalization of left ventricular function, should be expected.

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Main Authors: Amaral,Fernando, Carvalho,Julene S., Granzotti,João A., Shinebourne,Elliot A.
Format: Digital revista
Language:English
Published: Sociedade Brasileira de Cardiologia - SBC 1999
Online Access:http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X1999000300004
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spelling oai:scielo:S0066-782X19990003000042002-01-08Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatmentAmaral,FernandoCarvalho,Julene S.Granzotti,João A.Shinebourne,Elliot A. anomalous left coronary artery Bland-White-Garland syndrome left ventricular function OBJECTIVE: To report the authors' experience with the anomalous origin of the left coronary artery (AOLCA) from the pulmonary trunk, emphasizing preoperative data, surgical aspects and midterm results of the follow-up. METHODS: Retrospective analysis of 11 patients operated upon at the Royal Brompton Hospital from October, 84 to April, 97. RESULTS: Nine infants had heart failure (HF) and two other children presented with dyspnea and chest pain. All had ECG changes. The echocardiogram identified the anomalous origin of the coronary artery in 7 (64%) patients and hemodynamic studies were performed in 7 patients. All infants were operated upon between the 2nd and 10th month of life. Six patients were treated with aortic reimplantation of the left coronary artery, whereas five were operated upon according to the Takeuchi technique. All patients are alive, with clear improvement of the ECG changes and ventricular function, as evaluated by echocardiography. Two patients operated upon according to the Takeuchi technique required additional surgery due to severe supravalvular pulmonary stenosis. CONCLUSION: AOLCA is a rare disease. Most patients show early signs of severe HF associated with ECG findings. Surgical therapy must be instituted early in the disease, preferentially through aortic implantation of the anomalous coronary artery, with a high possibility of success. Shortly after surgery, clinical and ECG improvement, as well as normalization of left ventricular function, should be expected.info:eu-repo/semantics/openAccessSociedade Brasileira de Cardiologia - SBCArquivos Brasileiros de Cardiologia v.72 n.3 19991999-03-01info:eu-repo/semantics/articletext/htmlhttp://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X1999000300004en10.1590/S0066-782X1999000300004
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country Brasil
countrycode BR
component Revista
access En linea
databasecode rev-scielo-br
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region America del Sur
libraryname SciELO
language English
format Digital
author Amaral,Fernando
Carvalho,Julene S.
Granzotti,João A.
Shinebourne,Elliot A.
spellingShingle Amaral,Fernando
Carvalho,Julene S.
Granzotti,João A.
Shinebourne,Elliot A.
Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment
author_facet Amaral,Fernando
Carvalho,Julene S.
Granzotti,João A.
Shinebourne,Elliot A.
author_sort Amaral,Fernando
title Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment
title_short Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment
title_full Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment
title_fullStr Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment
title_full_unstemmed Anomalous origin of the left coronary artery from the pulmonary trunk. Clinical features and midterm results after surgical treatment
title_sort anomalous origin of the left coronary artery from the pulmonary trunk. clinical features and midterm results after surgical treatment
description OBJECTIVE: To report the authors' experience with the anomalous origin of the left coronary artery (AOLCA) from the pulmonary trunk, emphasizing preoperative data, surgical aspects and midterm results of the follow-up. METHODS: Retrospective analysis of 11 patients operated upon at the Royal Brompton Hospital from October, 84 to April, 97. RESULTS: Nine infants had heart failure (HF) and two other children presented with dyspnea and chest pain. All had ECG changes. The echocardiogram identified the anomalous origin of the coronary artery in 7 (64%) patients and hemodynamic studies were performed in 7 patients. All infants were operated upon between the 2nd and 10th month of life. Six patients were treated with aortic reimplantation of the left coronary artery, whereas five were operated upon according to the Takeuchi technique. All patients are alive, with clear improvement of the ECG changes and ventricular function, as evaluated by echocardiography. Two patients operated upon according to the Takeuchi technique required additional surgery due to severe supravalvular pulmonary stenosis. CONCLUSION: AOLCA is a rare disease. Most patients show early signs of severe HF associated with ECG findings. Surgical therapy must be instituted early in the disease, preferentially through aortic implantation of the anomalous coronary artery, with a high possibility of success. Shortly after surgery, clinical and ECG improvement, as well as normalization of left ventricular function, should be expected.
publisher Sociedade Brasileira de Cardiologia - SBC
publishDate 1999
url http://old.scielo.br/scielo.php?script=sci_arttext&pid=S0066-782X1999000300004
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